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Table 1 Characteristics of subjects

From: Increased task-uncorrelated muscle activity in childhood dystonia

(A) Children with dystonia
ID Sex Age Diagnosis Bad scale score DOM. Arm Medications
     R Arm L Arm Trunk Total   
d1 M 106 Idiopathic primary generalized dystonia; DYT1- 1.5 1.5 0.5 5.5 R Trihexyphenidyl (ARTANE), carbidopa-levodopa (SINEMET)
d2 M 234 Secondary generalized dystonia; mutation in TTPA (tocopherol transfer protein A) causing vitamin E deficiency 1.5 1.5 0.5 6 R Vit E, botulinum toxin injections on sternocleidomastoid (L and R), levator scapulae (R), scalenus medius (R) 4 months before the experiment
d3 F 123 Secondary hemidystonia; traumatic brain injury 3 2 0.5 5.5 L Trihexyphenidyl (ARTANE), Baclofen
d4 M 189 Primary segmental dystonia; DYT1- 1 1 0 2 L Trihexyphenidyl (ARTANE)
d5 F 221 Secondary generalized dystonia; perinatal hypoxic ischemic injury 3 3 0.5 8.5 R Trihexyphenidyl (ARTANE), carbidopa-levodopa (SINEMET)
d6 M 108 Secondary generalized dystonia; perinatal hypoxic ischemic injury 3 3 3 9* L Baclofen, botulinum toxin injections on Triceps (R), Biceps (R), and Flexor Carpi Ulnaris (R) 3 months before the experiment
d7 M 123 Secondary segmental dystonia; perinatal hypoxic ischemic injury 2.5 2.5 2 10 R No medication
(B) Control children
ID Sex Age   DOM. Arm  
c1 F 235   R  
c2 F 240   R  
c3 F 224   R  
c4 F 210   R  
c5 M 225   R  
c6 M 217   R  
c7 F 143   L  
c8 F 124   R  
c9 F 127   L  
  1. A: Children with dystonia. Subject ID; Sex; Age (months); Diagnosis; Severity of Right (R) Arm, Left (L) Arm, Trunk, and Total Score (scores averaged over two raters are based on the Barry-Albright Dystonia Scale [10]; for each segment the score ranges from 0 - absence of dystonia - to 4 - severe dystonia); Dominant arm; Medications. [*Total Score NOT available]
  2. B: Control children. Subject ID; Sex; Age (months); Dominant arm