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Table 1 Characteristics of subjects

From: Increased task-uncorrelated muscle activity in childhood dystonia

(A) Children with dystonia

ID

Sex

Age

Diagnosis

Bad scale score

DOM. Arm

Medications

    

R Arm

L Arm

Trunk

Total

  

d1

M

106

Idiopathic primary generalized dystonia; DYT1-

1.5

1.5

0.5

5.5

R

Trihexyphenidyl (ARTANE), carbidopa-levodopa (SINEMET)

d2

M

234

Secondary generalized dystonia; mutation in TTPA (tocopherol transfer protein A) causing vitamin E deficiency

1.5

1.5

0.5

6

R

Vit E, botulinum toxin injections on sternocleidomastoid (L and R), levator scapulae (R), scalenus medius (R) 4 months before the experiment

d3

F

123

Secondary hemidystonia; traumatic brain injury

3

2

0.5

5.5

L

Trihexyphenidyl (ARTANE), Baclofen

d4

M

189

Primary segmental dystonia; DYT1-

1

1

0

2

L

Trihexyphenidyl (ARTANE)

d5

F

221

Secondary generalized dystonia; perinatal hypoxic ischemic injury

3

3

0.5

8.5

R

Trihexyphenidyl (ARTANE), carbidopa-levodopa (SINEMET)

d6

M

108

Secondary generalized dystonia; perinatal hypoxic ischemic injury

3

3

3

9*

L

Baclofen, botulinum toxin injections on Triceps (R), Biceps (R), and Flexor Carpi Ulnaris (R) 3 months before the experiment

d7

M

123

Secondary segmental dystonia; perinatal hypoxic ischemic injury

2.5

2.5

2

10

R

No medication

(B) Control children

ID

Sex

Age

 

DOM. Arm

 

c1

F

235

 

R

 

c2

F

240

 

R

 

c3

F

224

 

R

 

c4

F

210

 

R

 

c5

M

225

 

R

 

c6

M

217

 

R

 

c7

F

143

 

L

 

c8

F

124

 

R

 

c9

F

127

 

L

 
  1. A: Children with dystonia. Subject ID; Sex; Age (months); Diagnosis; Severity of Right (R) Arm, Left (L) Arm, Trunk, and Total Score (scores averaged over two raters are based on the Barry-Albright Dystonia Scale [10]; for each segment the score ranges from 0 - absence of dystonia - to 4 - severe dystonia); Dominant arm; Medications. [*Total Score NOT available]
  2. B: Control children. Subject ID; Sex; Age (months); Dominant arm